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Audiology and Speech Research > Volume 12(Suppl 1); 2016 > Article
Audiology and Speech Research 2016;12(0): S10-S13.
Published online: March 31, 2016.
doi: http://doi.org/10.21848/asr.2016.12.S1.S10
청각신경병증의 치료
정성욱, 김이석
동아대학교 의과대학 이비인후과학교실
Management of Auditory Neuropathy Spectrum Disorder
Sung Wook Jeong, Lee-Suk Kim
Department of Otolaryngology, Dong-A University College of Medicine, Busan, Korea
Correspondence  Lee-Suk Kim ,Tel: +82-51-240-5428, Fax: +82-51-253-0712, Email: klsolkor@chol.com
Received: February 21, 2016;  Accepted: March 10, 2016.  Published online: March 31, 2016.
Auditory neuropathy spectrum disorder (ANSD) is a hearing disorder characterized by an absent or severely abnormal auditory brainstem response (ABR) with preservation of cochlear microphonics or otoacoustic emissions (OAE). These findings suggest that outer hair cell is normal but function of inner hair cell or auditory nerve is impaired. ANSD is a disorder in which behavioral threshold measures do not match with other measures of auditory function such as ABR data and speech discrimination scores. The patients with ANSD can have various hearing thresholds from normal to profound degree, but speech discrimination is very poor and out of proportion to pure tone loss. Therefore conventional amplification is of little benefit to improve speech-language ability. Frequency-modulation system to enhance signal-to-noise ratio can help in situations with background noise like classroom, car, and restaurant. Visual communication is also helpful. Cochlear implantation is a promising tool for habilitation of patients with ANSD. Most patients who receive cochlear implantation show significant improvements in speech perception abilities and good results in electrical ABR. However some very young children with ANSD can recover during first 12-18 months of life and develop speech and language normally without any intervention. Therefore cochlear implantation should be considered after the persistent ANSD is confirmed through repeated assessment using electrophysiological measures and behavioral hearing tests.
Key Words: Auditory neuropathy spectrum disorder, Cochlear implantation, Auditory brainstem response, Otoacoustic emission.
중심단어: 청각신경병증· 인공와우이식· 청성뇌간반응· 이음향방사.
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