KID 증후군 아동의 인공와우이식 후 청각수행력의 변화 |
이미숙1, 조수진2 |
1지음청각언어연구소 2대불대학교 언어치료청각학과 |
The Changes of Auditory Performance After Cochlear Implantation in
Child with KID syndrome |
Misook Lee1, Soojin Cho2 |
1Jeeum Auditory Rehabilitation Center, Daegu, Korea 2Department of Speech Pathology & Audiology, Daebul University, Yeongam, Korea |
Correspondence |
Soojin Cho ,Tel: (061) 469-1482, Fax: (061) 469-1317, Email: sj2434@db.ac.kr
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Received: May 2, 2011; Revised: June 2, 2011 Accepted: June 7, 2011. Published online: June 30, 2011. |
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ABSTRACT |
Keratitis-ichthyosis-deafness (KID) syndrome is a rare congenital ectodermal disorder, caused by heterozygous missense mutation in
GJB2, encoding the gap junction protein connexin 26. This case review focused on the auditory performance after cochlear
implantation for a child with KID syndrome. The average score of auditory performance improved steadily after the use of cochlear
implant and continued over for 12 months. Moreover, Six months after cochlear implantation, the subject showed a significant
improvement in auditory performance. In particular the score of Monosyllabic-Trochee-Polysyllabic word (MTP) was improved from
8.3% to 100% for 12 months. The results of this case suggested that auditory rehabilitation and cochlear implantation for a child with
KID syndrome would be effective and important. |
Key Words:
Auditory performance, Auditory-verbal approach, Cochlear implantation, KID syndrome. |
중심단어:
인공와우이식, 청각-구화법, 청각수행력, KID
증후군. |
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